Keywords

Cowden hamartoma tumor syndrome, genetic testing, hereditary cancer syndrome, Li-Fraumeni syndrome, Peutz-Jeghers syndrome, primary care nurse practitioner

Abstract

Hereditary cancer syndromes, resulting from mutations of tumor-suppressor genes, can significantly increase risk for breast cancer. While Hereditary Breast and Ovarian Cancer Syndrome caused by BRCA1/2 mutations is well known, less well-known hereditary cancer syndromes also exist. This clinical practice feature focuses on three other syndromes including, Li-Fraumeni, Cowden, and Peutz-Jeghers. This article will help prepare nurse practitioners to recognize key features of these syndromes and understand testing criteria. Additionally, this article discusses barriers to diagnosing hereditary cancer syndromes and the role of primary care nurse practitioners in ordering genetic tests and making genetic referrals for optimal patient care.

Document Type

Peer-Reviewed Article

Publication Date

2020-07-01

Language

English

College

Nursing

Department

Nursing

University Standing at Time of Publication

Graduate Student

Included in

Nursing Commons

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